INTRODUCTION :

Ebstein’s anomaly (EA) is a rare congenital heart defect usually presenting around birth years, where in the septal and posterior leaflets of the tricuspid valve are displaced towards the apex of the right ventricle, atrializing the right ventricle. Although it accounts for only about 0.5% of congenital heart defects, only 5% of patients are known to survive beyond the fifth decade of life. [1] We present the case report of a patient with Ebstein’s anomaly surpassing the sixth decade of life highlighting the importance of regular cardiac surveillance enabling increased lifespan of patients with the disease.

REFERENCES :

1) SURPASSING THE FIFTH DECADE: EBSTEIN’S ANOMALY CASE REPORT – CHEST (chestnet.org)
2) Mulla S, Asuka E, Bora V, Siddiqui WJ. StatPearls [Internet]. StatPearls Publishing; Treasure Island (FL): Jan 8, 2024. Tricuspid Regurgitation. [PubMed]
3) Attenhofer Jost CH, Connolly HM, Dearani JA, Edwards WD, Danielson GK. Ebstein’s anomaly. Circulation. 2007 Jan 16;115(2):277-85. [PubMed]
4) Mazurak M, Kusa J. The Two Anomalies of Wilhelm Ebstein. Tex Heart Inst J. 2017 Jun;44(3):198-201. [PMC free article] [PubMed]
5) Holst KA, Connolly HM, Dearani JA. Ebstein’s Anomaly. Methodist Debakey Cardiovasc J. 2019 Apr-Jun;15(2):138-144. [PMC free article] [PubMed]
6) Dearani JA, Mora BN, Nelson TJ, Haile DT, O’Leary PW. Ebstein anomaly review: what’s now, what’s next? Expert Rev Cardiovasc Ther. 2015 Oct;13(10):1101-9. [PubMed]
7) Anderson KR, Zuberbuhler JR, Anderson RH, Becker AE, Lie JT. Morphologic spectrum of Ebstein’s anomaly of the heart: a review. Mayo Clin Proc. 1979 Mar;54(3):174-80. [PubMed]
8) Fuchs MM, Connolly HM. Ebstein Anomaly in the Adult Patient. Cardiol Clin. 2020 Aug;38(3):353-363. [PubMed]
9) Ebstein Anomaly and Malformation – StatPearls – NCBI Bookshelf (nih.gov)
10) Oxenius A, Attenhofer Jost CH, Prêtre R, Dave H, Bauersfeld U, Kretschmar O, Seifert B, Balmer C, Valsangiacomo Buechel ER. Management and outcome of Ebstein’s anomaly in children. Cardiol Young. 2013 Feb;23(1):27-34. [PubMed]